ATHENA #349 ATAXIA, FRIEDREICH(FXN) EVALUATION

Message
QUEST-> ATHENA LABS


Test Code
ATHENA #349


CPT Codes
81286,81284

Includes

Friedreich Ataxia (FXN) DNA Sequencing Test
Friedreich Ataxia (FXN) Repeat Expansion Test


Preferred Specimen
WHOLE BLOOD


Minimum Volume
8mLs


Instructions
DRAW 2 LAV TOP TUBES.*** PATHOLOGIST MUST APPROVE TEST PRIOR TO SENDING OUT.


Transport Container
ORIGINAL TUBES


Transport Temperature
REFRIGERATED


Specimen Stability
Room temperature: 10 days, Refrigerated: 10 days, Frozen: Unacceptable


Methodology
Next Generation Sequencing, Repeat Expansion Detection by PCR, Southern Blot

Report Available
21-28 DAYS


Reference Range
No sequence variants detected or expansions outside of the normal range


Clinical Significance
Detection of sequence variants and expansions of FXN

Typical Presentation: Children and Adults: Ataxia, dysarthria, muscle weakness, spasticity in the lower limbs, areflexia, cardiomyopathy, diabetes mellitus

Indications for testing: Clinical features consistent with those of Friedreich's Ataxia
Higher blood volumes ensure adequate DNA quantity, which varies with WBC, specimen condition, and need for confirmatory testing. Patients, 0-3 years have higher WBC, yielding more DNA per mL of blood


Performing Laboratory
ATHENA DIAGNOSTICS 200 Forest Street, 2nd Floor Marlborough, MA 01752 Phone (508) 756-2886

Additional Information
ATAXIA, FRIEDREICH(FXN) EVALUATION


The CPT Codes provided in this document are based on AMA guidelines and are for informational purposes only. CPT coding is the sole responsibility of the billing party. Please direct any questions regarding coding to the payor being billed. Any Profile/panel component may be ordered separately. Reflex tests are performed at an additional charge.